Liver Transplantation Review

These results indicate that liver transplantation can cure not only genetic disorders that present in the liver, but also liver disorders associated with extrahepatic pathology. Furthermore, a genetic defect present in all body cells such as familial hypercholesterolemia can be compensated by the mass of normal cells provided by liver transplantation.

Cholesterol Ester Storage Disease

 Cirrhosis is a possible complication and was successfully treated by liver transplantation in a 14-year-old child. Neonatal Hemochromatosis. A few infants received liver transplantation with success. The recent availability of medical antioxidant therapy may limit the need for transplantation in the future.

Type IV Glycogen Storage Disease

Liver transplantation eliminates cirrhosis and may even improve the degree of amylopectin storage in the heart. Careful follow-up is, however, necessary in this respec.