Monday, November 29, 2010

Type IV Glycogen Storage Disease

Liver transplantation eliminates cirrhosis and may even improve the degree of amylopectin storage in the heart. Careful follow-up is, however, necessary in this respec.

Type IA and IB Glycogen Storage Diseases

Beside severe hypoglycemia, growth failure, and acidosis, they also carry a risk of liver adenoma, possibly complicated by intratumoral hemorrhage or liver cell carcinoma.

Wilson's Disease

This is usually treated successfully with copper-chelating agents; in a few cases, howover (e.g., acure liver failure with or without hemolysis, acute relapse after discontinuation of therapy),