Hereditary Tyrosinemia

For several years, liver transplantation has proven extremely useful in children with this otherwise lethal disease. The recenr introduction of the enzyme inhibitor NTBC (see chapter by Kvitington, Clayton, and Leonard, this volume), may diminish the need for liver transplantation.

Add caption

So far, however, liver transplantation remains indicated in children with cirrhosis above the age of 2 because of the high risk of hepatocellular carcinoma after this age and of the lack of data concerning the afficacy of NTBC for its prevention.

Genetic Epidemiology of Cancer	Customer Review: Click Here for More Info	$484.00
Inborn Metabolic Diseases: Diagnosis and Treatment	Customer Review: Click Here for More Info	$173.74
Liver Disease in Children	Customer Review: Click Here for More Info	$174.68
Inherited Metabolic Diseases: A Clinical Approach	Customer Review: Click Here for More Info	$93.18
Nutrition Management of Patients With Inherited Metabolic Diseases	Customer Review: Click Here for More Info	$95.96